A Case of Senile Langerhans Cell Histiocytosis with Soft Tissue Mass as the Main Manifestation

XING Mingquan; WU Weixia; SUN Xiaoxing; WANG Qikai; HAN Hao; GE Hongfeng

doi:10.12376/j.issn.2097-0501.2023.03.015

Journal of Rare Diseases > 2023 > 2(3): 432-435. > DOI: 10.12376/j.issn.2097-0501.2023.03.015

XING Mingquan, WU Weixia, SUN Xiaoxing, WANG Qikai, HAN Hao, GE Hongfeng. A Case of Senile Langerhans Cell Histiocytosis with Soft Tissue Mass as the Main Manifestation[J]. Journal of Rare Diseases, 2023, 2(3): 432-435. DOI: 10.12376/j.issn.2097-0501.2023.03.015

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A Case of Senile Langerhans Cell Histiocytosis with Soft Tissue Mass as the Main Manifestation

1.
Department of Hematology, the People′s Hospital of Bozhou City in Anhui Province, Bozhou 236800, China
2.
Image Center, the People′s Hospital of Bozhou City in Anhui Province, Bozhou 236800, China

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Corresponding author:
GE Hongfeng, E-mail: ghfzz@163.com
Received Date: June 21, 2022
Accepted Date: December 20, 2022
Available Online: September 08, 2023

Graphical Abstract

Abstract

Abstract

Langerhans cell histiocytosis (LCH) is a rare disease characterized by the proliferation of Langerhans cells and the destruction of local tissue. LCH large occurs in children, whilst incidence of the elderly population is extremely low, and there are few related studies. LCH lesions can involve multiple organs and systems, including bone tissue, lymph nodes, skin, liver, and spleen. However, it is rare that multiple soft tissues are implicated for eldly patients with LCH and present with soft tissue mass as the main manifestation. Here is a report on the clinical features, treatment and prognosis of an elderly LCH with multiple soft tissue masses as the main manifestation, in order to provide clinical reference.
- Langerhans cell histiocytosis,
- soft tissue mass,
- rare diseases

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References (16)

References

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A Case of Senile Langerhans Cell Histiocytosis with Soft Tissue Mass as the Main Manifestation