Abstract: Hepatic angiosarcoma is a rare, highly malignant tumor originating from liver blood vessels or lymphatic vessels. Its clinical manifestations and imaging examinations are not specific, and pathological biopsy is needed to confirm the diagnosis. This article reports a 47-year-old male patient with hepatic angiosarcoma, who has clinical manifestations of abdominal pain, jaundice, and disseminated intravascular coagulation. The CT and MRI findings of this patient are similar to hepatic sinusoidal obstruction syndrome. Relevant literature on hepatic angiosarcoma in recent years was reviewed. The manifestations, diagnosis and treatment of hepatic angiosarcoma were summarized to improve clinicians' understanding of the disease.